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Have you heard on the ulnar dimelia or mirror hand syndrome

ulnar dimelia

Ulnar dimelia (reflect disfigurement) is an uncommon dysontogenetic deformation of the upper appendage brought about by an embryonic unsettling influence of creating appendage bud. It is described by two ulnae, the duplication of the ulnar parts of the carpus, metacarpals, and phalanges, with the nonattendance of the span and thumb. It is normally one-sided. This inconsistency might be related with shoulder

disengagement, fibular dimelia, idiopathic scoliosis, cirrhosis, pyloric hypertrophy or a polycystic kidney Around 72 cases have been accounted for since it was first depicted in
1587 1-3. We in this portray an uncommon instance of ulnar dimelia related to ipsilateral polydactyly.

Case Report

A 2-year-old young lady gave six digits on her correct hand. She was conceived at term after an uneventful pregnancy.
She was the main tyke. The two guardians were solid and did not have any appendage variations from the norm. Family ancestry was unremarkable. The chromosomal examination demonstrated an ordinary 46, XX

karyotype Every single physical finding was ordinary with the exception of the correct upper appendage, described by a correct lower arm that was shorter than the left lower arm Wrist developments were ordinary.

Flexion of the elbow and supination/pronation of lower arm were constrained to 40 degrees, what’s more, 10 degrees, separately. There were no apparent nasal, auricular or facial variations from the norm. Her psychomotor improvement was

was ordinary. The single physiological refinement was that her correct hand had six fingers and no thumb. Radiographs of the correct lower arm and hand demonstrated ulnar duplication, nonattendance of the sweep and thumb,
lower humerus articulating with two olecranon forms, and symmetric polydactyly (Figure 1). Her folks rejected careful treatment.

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