Ulnar dimelia (reflect disfigurement) is an uncommon dysontogenetic deformation of the upper appendage brought about by an embryonic unsettling influence of creating appendage bud. It is described by two ulnae, the duplication of the ulnar parts of the carpus, metacarpals, and phalanges, with the nonattendance of the span and thumb. It is normally one-sided. This inconsistency might be related with shoulder
disengagement, fibular dimelia, idiopathic scoliosis, cirrhosis, pyloric hypertrophy or a polycystic kidney Around 72 cases have been accounted for since it was first depicted in
1587 1-3. We in this portray an uncommon instance of ulnar dimelia related to ipsilateral polydactyly.
A 2-year-old young lady gave six digits on her correct hand. She was conceived at term after an uneventful pregnancy.
She was the main tyke. The two guardians were solid and did not have any appendage variations from the norm. Family ancestry was unremarkable. The chromosomal examination demonstrated an ordinary 46, XX
karyotype Every single physical finding was ordinary with the exception of the correct upper appendage, described by a correct lower arm that was shorter than the left lower arm Wrist developments were ordinary.
Flexion of the elbow and supination/pronation of lower arm were constrained to 40 degrees, what’s more, 10 degrees, separately. There were no apparent nasal, auricular or facial variations from the norm. Her psychomotor improvement was
was ordinary. The single physiological refinement was that her correct hand had six fingers and no thumb. Radiographs of the correct lower arm and hand demonstrated ulnar duplication, nonattendance of the sweep and thumb,
lower humerus articulating with two olecranon forms, and symmetric polydactyly (Figure 1). Her folks rejected careful treatment.
- Harrison RG, Pearson Mama, Roaf R. Ulna dimelia. J Bone Joint Surg Br 1960; 42: 549-55.
- Harpf C, Hussl H. An instance of mirror hand distortion with a 17-year postoperative development. Case report.
Scand J Plast Reconstr Hand Surg 1999; 33: 329–33.
- Upton J. Innate peculiarities of the hand and lower arm. In: McCarthy JG, ed. Plastic medical procedure.
Philadelphia: WB Saunders, 1990: 5356–62.
- Gorriz G. Ulnar dimelia- – an appendage without anteroposterior separation. J Hand Surg Am 1982; 7: 466-69.
- Ueshima T, Uehara M. Ulnar dimelia in a calf. Japanese Diary of Veterinary Science 1981; 43: 351-57.
- Sandrow RE, Sullivan PD, Steel HH. Genetic ulnar and fibular dimelia with unconventional facies. J Bone
Joint Surg Br 1970; 52: 367-71.
- Laurin CA, Favreau JC, Labelle P. Respective nonattendance of the sweep and tibia with two-sided reduplication of the ulna and fibula. J Bone Joint Surg Br 1964; 46: 137-42.
- Green DP, Hotchkiss RN, Pederson WC. Ulna dimelia. Green’s usable hand medical procedure, fourth end, 1999,
- Muteti EN, Carter LL. Mirror Hand (Ulna Dimelia): A Case Report. East and Focal African J Surg
segmental Laurin-Sandrow disorder. Am J Medications Genet A 2004; 131: 77-81.